Author(s): Jatin Arora, Kirti Jain, Usha D.S., Mahesh N.M.

Email(s): jatinarora1310@gmail.com

DOI: 10.52711/2231-5713.2024.00040   

Address: Jatin Arora*, Kirti Jain, Usha D.S., Mahesh N.M.
Pharm. D. Intern, KLE College of Pharmacy, 968 FF Ranibagh, Pitampura, Delhi - 110034, India.
*Corresponding Author

Published In:   Volume - 14,      Issue - 3,     Year - 2024


ABSTRACT:
Ebstein's anomaly is a rare congenital heart condition, occurring in only 1 to 5 out of every 200,000 live births, accounting for less than 1% of all cases of congenital heart defects. This anomaly is characterized by the downward displacement of the septal leaflet of the tricuspid valve and the presence of an atrialized right ventricle. Our patient, an eleven-year-old girl, initially presented with symptoms such as chest pain, shortness of breath, and hemoptysis (blood vomiting). Upon examination, we identified moderate tricuspid valve regurgitation and observed an enlarged, globe-shaped heart, which led us to diagnose the child with Ebstein's anomaly. Additionally, the presence of Escherichia coli in her blood resulted in sepsis. Given the patient's overall condition, cardiovascular surgery was not considered, and she was instead provided with symptomatic treatment. This case report highlights the possibility of successful pediatric outcomes in complex congenital heart diseases, emphasizing the need for individualized surgical treatment plans.


Cite this article:
Jatin Arora, Kirti Jain, Usha D.S., Mahesh N.M.. Case Report on Ebstein’s Anomaly with Hemoptysis and Sepsis in Eleven Years Old Girl. Asian Journal of Pharmacy and Technology. 2024; 14(3):247-0. doi: 10.52711/2231-5713.2024.00040

Cite(Electronic):
Jatin Arora, Kirti Jain, Usha D.S., Mahesh N.M.. Case Report on Ebstein’s Anomaly with Hemoptysis and Sepsis in Eleven Years Old Girl. Asian Journal of Pharmacy and Technology. 2024; 14(3):247-0. doi: 10.52711/2231-5713.2024.00040   Available on: https://ajptonline.com/AbstractView.aspx?PID=2024-14-3-9


REFERENCES:
1.    Dearani JA, Danielson GK. Surgical management of Ebstein’s anomaly in the adult. In Seminars in Thoracic and Cardiovascular Surgery. 2005 Jun 1 (Vol. 17, No. 2, pp. 148-154). WB Saunders.
2.    Nihoyannopoulos P, McKenna WJ, Smith G, Foale R. Echocardiographic assessment of the right ventricle in Ebstein's anomaly: relation to clinical outcome. Journal of the American College of Cardiology. 1986; Sep 1; 8(3): 627-35.
3.    Paterick TE, Gerber TC, Pradhan SR, Lindor NM, Tajik AJ. Left ventricular noncompaction cardiomyopathy: what do we know?. Reviews in Cardiovascular Medicine. 2010; Jan 1; 11(2) :92-9.
4.    Celermajer DS, Cullen S, Sullivan ID, Spiegelhalter DJ, Wyse RK, Deanfield JE. Outcome in neonates with Ebstein's anomaly. Journal of the American College of Cardiology. 1992 Apr 1; 19(5): 1041-6.
5.    Yetman AT, Freedom RM, McCrindle BW. Outcome in cyanotic neonates with Ebstein’s anomaly. The American Journal of Cardiology. 1998 Mar 15; 81(6): 749-54.
6.    Shinkawa T, Polimenakos AC, Gomez-Fifer CA, Charpie JR, Hirsch JC, Devaney EJ, Bove EL, Ohye RG. Management and long-term outcome of neonatal Ebstein anomaly. The Journal of Thoracic and Cardiovascular Surgery. 2010; Feb 1; 139(2): 354-8.
7.    Bove EL, Hirsch JC, Ohye RG, Devaney EJ. How I manage neonatal Ebstein's anomaly. InSeminars in Thoracic and Cardiovascular Surgery: Pediatric Cardiac Surgery Annual. 2009; Jan 1 (Vol. 12, No. 1, 63-65). WB Saunders.
8.    Jost CH, Connolly HM, O'Leary PW, Warnes CA, Tajik AJ, Seward JB. Left heart lesions in patients with Ebstein anomaly. InMayo Clinic Proceedings. 2005; Mar 1 (Vol. 80, No. 3, 361-368). Elsevier.
9.    Miller MS, Rao PN, Dudovitz RN, Falk RE. Ebstein anomaly and duplication of the distal arm of chromosome 15: report of two patients. American Journal of Medical Genetics Part A. 2005; Dec 1; 139(2): 141-5.
10.    DW B. Mutations in the cardiac transcription factor NKX2. 5 affect diverse cardiac developmental pathways. J Clin Invest. 1999; 104: 1567-73.
11.    Choi R, Lee SK, Moon HS, Park IC, Hyun C. Ebstein’s anomaly with an atrial septal defect in a jindo dog. The Canadian Veterinary Journal. 2009; Apr; 50(4): 405.
12.    Haïssaguerre M, Shah DC, Jaïs P, Shoda M, Kautzner J, Arentz T, Kalushe D, Kadish A, Griffith M, Gaïta F, Yamane T. Role of Purkinje conducting system in triggering of idiopathic ventricular fibrillation. The Lancet. 2002; Feb 23; 359(9307): 677-8.
13.    Chauvaud S, Berrebi A, d'Attellis N, Mousseaux E, Hernigou A, Carpentier A. Ebstein's anomaly: repair based on functional analysis. European Journal of Cardio-thoracic Surgery. 2003; Apr 1; 23(4): 525-31.
14.    Nam SJ, Choi R, Park IC, Hyun CB. Tricuspid valve dysplasia complicated with pulmonic regurgitation in a Cocker Spaniel dog. Korean Journal of Veterinary Research. 2008; Dec; 48(4): 481-7.
15.    Atiq M, Lai L, Lee KJ, Benson LN. Transcatheter closure of atrial septal defects in children with a hypoplastic right ventricle. Catheterization and Cardiovascular Interventions. 2005; Jan; 64(1): 112-6.
16.    Calderón JE, Juárez GM, Pérez TA, Castillo JL, Miranda RS, Ramírez H, Amaya A. Percutaneous closure of patent foramen ovale with amplatzer device. Report of two cases. Archivos de cardiología de México. 2005;75(3):306-9.
17.    Hiramatsu Y, Noma M, Horigome H, Takahashi‐Igari M, Sakakibara Y. Biventricular repair of Ebstein's anomaly with pulmonary atresia in a low birth weight neonate. Journal of Cardiac Surgery. 2006; Jul; 21(4): 421-2.

Recomonded Articles:

Author(s): Goli Venkateshwarlu, Ragya Eslavath, Anasuri Santhosh, Gutha Suma, J.Venkanna, Y.Swetha

DOI:         Access: Open Access Read More

Author(s): S.K. Purohit, R. Solanki, R. Soni, V. Mathur

DOI:         Access: Open Access Read More

Author(s): R. Solanki, B.P. Nagori

DOI:         Access: Open Access Read More

Author(s): S. Janet Beula, Dr. R. Suthakaran, M. Bhanu Prakash, G. Sreeya, P. Pavan Kalyan, P. Shiva Prasad

DOI: 10.5958/2231-5713.2020.00016.1         Access: Open Access Read More

Author(s): P. Geetha, M. Varaprasannarao, D. Subalakshmi, R. V. Bibi Bergin

DOI: 10.52711/2231-5713.2022.00021         Access: Open Access Read More

Author(s): Jyotsna Anandrao Saonere, M. A. Channawar, Nitin I. Kochar, Deepak Mohale, Anil V Chandewar

DOI: 10.52711/2231-5713.2023.00015         Access: Closed Access Read More

Author(s): Vedanshu Malviya, Prashant Ajmire, Snehal Manekar, Gaurav Ingle, Pramod Burakle

DOI: 10.52711/2231-5713.2024.00017         Access: Closed Access Read More

Author(s): Jatin Arora, Kirti Jain, Usha D.S., Mahesh N.M.

DOI: 10.52711/2231-5713.2024.00040         Access: Closed Access Read More

Asian Journal of Pharmacy and Technology (AJPTech.) is an international, peer-reviewed journal, devoted to pharmaceutical sciences...... Read more >>>

RNI: Not Available                     
DOI: 10.5958/2231–5713 


Recent Articles




Tags